SYNDROMATIC HEPATIC DUCTULAR HYPOPLASIS (ALLAGILLE SYNDROME) IN A NIGERIAN : A CASE REPORT

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ABSTRACT

We report what, as far as we are aware, is the first documented case of Alagille syndrome which is characterized by chronic cholestasis. characteristic facies, pulmonary stenosis and defects at' the vertebral arch, in a Nigerian girl who presented at the age of two days and was followed up intermittently for a period or 10.5 years.

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